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Langerhans cell histiocytosis (LCH) in adults is a rare disorder that occurs when the body produces too many Langerhans cells (histiocytes), which are a type of white blood cell that helps fight infection.
1 sie 2023 · Histiocytosis refers to many rare blood disorders where white blood cells (histiocytes) build up in tissue. This includes conditions that range from mild and asymptomatic to potentially fatal. Everyone with histiocytosis has excess histiocytes in tissue that cause inflammation.
Langerhans cell histiocytosis is a rare clonal disease characterized by the proliferation of CD1a-positive immature dendritic cells. The purpose of this article was to present an updated review of recent advances in the pathogenesis, clinical features, imaging and treatment of this disease.
Background: Langerhans cell histiocytosis (LCH) is a proliferative disorder predominantly found in children. It often presents with pain in calvarium or spine and may cause neuroendocrine symptoms. The gold standard for diagnosing LCH is the detection of Birbeck Granules by EM.
Histiocytosis, also referred to as Langerhans Cell Histiocytosis (LCH), and formally called Histiocytosis X, represents a group of rare disorders involving specific cells that normally have important roles as part of the immune system.
1 mar 1987 · This article acts as an overview of this issue of Hematology/ Oncology Clinics of North America. We discuss the several themes that recur in the research and therefore in this issue concerning histiocytosis-X.
23 kwi 2021 · Histiocytoses constitute a heterogeneous group of rare disorders, characterised by infiltration of almost any organ by myeloid cells with diverse macrophage or dendritic cell phenotypes. Histiocytoses can start at any age. Diagnosis is based on histology in combination with appropriate clinical and radiological findings.
