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6 mar 2019 · The hepatic glycogen storage diseases (GSDs) are a group of disorders where abnormal storage or release of glycogen leads to potentially life-threatening hypoglycemia and metabolic disturbances. Dietary interventions have markedly improved the outcome for these disorders, from a previously fatal condition to one where people can do well with ...
1 mar 2020 · The hepatic glycogen storage diseases (GSDs) are a group of disorders where abnormal storage or release of glycogen leads to potentially life-threatening hypoglycemia and metabolic disturbances.
1 mar 2020 · Dietary interventions have markedly improved the outcome for these disorders, from a previously fatal condition to one where people can do well with proper care. This article chronicles the evolution of dietary management and treatment of the hepatic GSDs (types 0, I, III, VI, IX, and XI).
The hepatic glycogen storage diseases (GSDs) are a group of disorders where abnormal storage or release of glycogen leads to potentially life-threatening hypoglycemia and metabolic disturbances.
6 lis 2014 · Glycogen storage disease type I (GSD I) is a rare disease of variable clinical severity that primarily affects the liver and kidney.
7 wrz 2023 · Some GSDs have available guidelines for diagnosis and management. Diagnostic considerations include phenotypic characterization, biomarkers, imaging, genetic testing, enzyme activity analysis and...
12 sie 2014 · Fruits, juice, and other sucrose-containing, fructose-containing, and lactose-containing foods are limited or omitted. Spoon-feeding, drinking from a cup, and the introduction of table foods should follow the normal feeding progression in order to prevent long-term feeding disorders.
